This is an update to the 2014 Canadian Hereditary Angioedema Guideline with an
expanded scope to include the management of hereditary angioedema (HAE) patients …

Combinations of proinflammatory and procoagulant reactions are the unifying principle for a
variety of disorders affecting the cardiovascular system. The factor XII–driven contact system …

Hereditary Angioedema (HAE) is a rare and disabling disease for which early diagnosis and
effective therapy are critical. This revision and update of the global WAO/EAACI guideline on …

Hereditary Angioedema (HAE) is a rare and disabling disease. Early diagnosis and
appropriate therapy are essential. This update and revision of the global guideline for HAE …

Background Hereditary angioedema (HAE) is a rare genetic disease usually caused by
mutation in the C1 inhibitor or the coagulation Factor XII gene. However, in a series of …

Background Hereditary angioedema (HAE) with normal C1 inhibitor (C1-INH)(HAEnCI) is
associated with skin swellings, abdominal attacks, and the risk of asphyxia due to upper …

A myoferlin gain-of-function variant associates with a new type of hereditary angioedema A
myoferlin gain-of-function variant associates with a new type of hereditary angioedema …

Background The consensus documents published to date on hereditary angioedema with
C1 inhibitor deficiency (C1‐INH‐HAE) have focused on adult patients. Many of the previous …

Hereditary angioedema is a rare inherited disorder characterized by recurrent episodes of
the accumulation of fluids outside of the blood vessels, causing rapid swelling of tissues in …

Abstract Background Bradykinin-mediated angioedema (Bk-AE) can be life-threatening and
requires specific targeted therapies. Knowledge of its epidemiology may help optimize its …