Aim Fontan surgery is often the procedure of choice for patients with congenital single
effective ventricle. In the long term, elevated systemic venous pressure and chronic ischemia …

Background Fontan-associated liver disease (FALD) is universal in patients with a Fontan
circulation. Hepatocellular carcinoma (HCC) is one of its severe expressions, and, though …

We herein report three patients with Fontan-associated liver disease (FALD) who developed
hepatocellular carcinoma (HCC). All three patients had very high serum alpha-fetoprotein …

Heterotaxy syndrome is a rare congenital defect of left-right laterality of major visceral
organs, often categorised by the presence of symmetric left or right atrial heart chambers …

Advances in management of single ventricle cardiac physiology have increased life
expectancy in these patients from a matter of months or years to decades. The reversion of …

Background: Hepatocellular carcinoma (HCC) is more likely to occur in patients with a
history of Fontan surgery, possibly due to long-term liver congestion. Proton beam therapy …