[HTML][HTML] Desmoplastic small round cell tumor: a review of main molecular abnormalities and emerging therapy

CA Mello, FAB Campos, TG Santos, MLG Silva… - Cancers, 2021‏ - mdpi.com
Simple Summary Desmoplastic small round cell tumor is a rare neoplasm with extremely
aggressive behavior. Despite the multimodal treatment for newly diagnosed patients with …

Integrative genomic and transcriptomic analysis of leiomyosarcoma

P Chudasama, SS Mughal, MA Sanders… - Nature …, 2018‏ - nature.com
Leiomyosarcoma (LMS) is an aggressive mesenchymal malignancy with few therapeutic
options. The mechanisms underlying LMS development, including clinically actionable …

An update on emerging drugs in osteosarcoma: towards tailored therapies?

CM Hattinger, MP Patrizio, F Magagnoli… - Expert opinion on …, 2019‏ - Taylor & Francis
Introduction: Current treatment of conventional and non-conventional high-grade
osteosarcoma (HGOS) is based on the surgical removal of primary tumor and, when …

Patient-specific sarcoma organoids for personalized translational research: unification of the operating room with rare cancer research and clinical implications

SD Forsythe, H Sivakumar, RA Erali, N Wajih… - Annals of surgical …, 2022‏ - Springer
Introduction Sarcoma clinical outcomes have been stagnant for decades due to
heterogeneity of primaries, lack of comprehensive preclinical models, and rarity of disease …

Reading ADP-ribosylation signaling using chemical biology and interaction proteomics

KW Kliza, Q Liu, LWM Roosenboom, PWTC Jansen… - Molecular cell, 2021‏ - cell.com
ADP-ribose (ADPr) readers are essential components of ADP-ribosylation signaling, which
regulates genome maintenance and immunity. The identification and discrimination …

Trabectedin and olaparib in patients with advanced and non-resectable bone and soft-tissue sarcomas (TOMAS): an open-label, phase 1b study from the Italian …

G Grignani, L D'Ambrosio, Y Pignochino… - The Lancet …, 2018‏ - thelancet.com
Background Trabectedin is an alkylating drug with a unique mechanism of action causing
single-strand and double-strand DNA breaks that activate DNA damage-response …

Analysis of mutational signatures with yet another package for signature analysis

D Hübschmann, L Jopp‐Saile… - Genes …, 2021‏ - Wiley Online Library
Different mutational processes leave characteristic patterns of somatic mutations in the
genome that can be identified as mutational signatures. Determining the contributions of …

[HTML][HTML] Identification of differentially expressed genes between original breast cancer and xenograft using machine learning algorithms

D Wang, JR Li, YH Zhang, L Chen, T Huang, YD Cai - Genes, 2018‏ - mdpi.com
Breast cancer is one of the most common malignancies in women. Patient-derived tumor
xenograft (PDX) model is a cutting-edge approach for drug research on breast cancer …

Bone sarcomas in the immunotherapy era

MF Heymann, K Schiavone… - British Journal of …, 2021‏ - Wiley Online Library
Bone sarcomas are primary bone tumours found mainly in children and adolescents, as
osteosarcoma and Ewing's sarcoma, and in adults in their 40s as chondrosarcoma. The last …

[HTML][HTML] Targeted and immuno-based therapies in sarcoma: mechanisms and advances in clinical trials

F Tang, Y Tie, YQ Wei, CQ Tu, XW Wei - Biochimica et Biophysica Acta …, 2021‏ - Elsevier
Sarcomas represent a distinct group of rare malignant tumors with high heterogeneity.
Limited options with clinical efficacy for the metastatic or local advanced sarcoma existed …