Use of next-generation sequencing for identifying mitochondrial disorders

S Mahmud, S Biswas, S Afrose, MA Mita… - Current Issues in …, 2022‏ - mdpi.com
Mitochondria are major contributors to ATP synthesis, generating more than 90% of the total
cellular energy production through oxidative phosphorylation (OXPHOS): metabolite …

Hearing Loss: Genetic Testing, Current Advances and the Situation in Latin America

MA De Rosa, MT Bernardi, S Kleppe, K Walz - Genes, 2024‏ - mdpi.com
Congenital hearing loss is the most common birth defect, estimated to affect 2–3 in every
1000 births, with~ 50–60% of those related to genetic causes. Technological advances …

Genetic etiology of non-syndromic hearing loss in Latin America

K Lezirovitz, RC Mingroni-Netto - Human Genetics, 2022‏ - Springer
Latin America comprises all countries from South and Central America, in addition to
Mexico. It is characterized by a complex mosaic of regions with heterogeneous genetic …

[HTML][HTML] Global prevalence of the mitochondrial MT-RNR1 A1555G variant in non-syndromic hearing loss: A systematic review and meta-analysis

B Han, W Wang, H Wu, J Hu, L Sun, Y Zhu, AG Cheng… - Neuroscience, 2025‏ - Elsevier
Non-syndromic sensorineural hearing loss (NSHL) significantly affects quality of life and is
often associated with the MT-RNR1 A1555G variant. This meta-analysis investigated the …

Genetic epidemiology of mitochondrial pathogenic variants causing nonsyndromic hearing loss in a large cohort of South Indian hearing impaired individuals

M Subathra, A Ramesh, M Selvakumari… - Annals of Human …, 2016‏ - Wiley Online Library
Mitochondria play a critical role in the generation of metabolic energy in the form of ATP.
Tissues and organs that are highly dependent on aerobic metabolism are involved in …

Analysis of mitochondrial alterations in Brazilian patients with sensorineural hearing loss using MALDI-TOF mass spectrometry

RM Alves, SM da Silva Costa… - BMC medical …, 2016‏ - Springer
Background Mutations in the mitochondrial DNA (mtDNA) have been associated with
aminoglycoside-induced and nonsyndromic deafness in different populations. In the present …

Development and application of a rapid and sensitive genoty** method for pharmacogene variants using the single-stranded tag hybridization chromatographic …

M Kumondai, A Ito, E Hishinuma, A Kikuchi… - Drug metabolism and …, 2018‏ - Elsevier
Genetic polymorphisms contribute to inter-individual variability in the metabolism of multiple
clinical drugs, including warfarin, thiopurines, primaquine, and aminoglycosides. A rapid …

The mitochondrial transfer RNAAsp A7551G mutation may contribute to the clinical expression of deafness associated with the A1555G mutation in a pedigree with …

J Zhang, B Lu, WW **a, B Fang… - Molecular …, 2019‏ - spandidos-publications.com
The role of mitochondrial (mt) DNA variations in hearing loss have been studied extensively;
in particular, the well‑known pathogenic A1555G mutation in the human mitochondrial 12S …

[PDF][PDF] A szenzorineurális halláscsökkenés genetikai hátterének vizsgálata

N Kecskeméti - 2019‏ - repo.lib.semmelweis.hu
Veleszületett halláscsökkenés minden 1000 újszülöttből 1-3 esetben fordul elő, míg a
koraszülöttek esetén ez az arány a 4-5‰-et is elérheti. A veleszületett halláscsökkenések …

Características de la hipoacusia en pacientes con la mutación a1555g del gen mtrnr1

A Carrancho García - 2016‏ - repositorio.unican.es
Introducción: La mutación A1555G del gen MTRNR1 del ADN mitocondrial es responsable
del 20% de todos los casos familiares de hipoacusia neurosensorial bilateral no sindrómica …