Advances in progressive supranuclear palsy: new diagnostic criteria, biomarkers, and therapeutic approaches

AL Boxer, JT Yu, LI Golbe, I Litvan, AE Lang… - The Lancet …, 2017 - thelancet.com
Progressive supranuclear palsy (PSP), previously believed to be a common cause of
atypical parkinsonism, is now recognised as a range of motor and behavioural syndromes …

Evolving concepts in progressive supranuclear palsy and other 4-repeat tauopathies

M Stamelou, G Respondek, N Giagkou… - Nature Reviews …, 2021 - nature.com
Tauopathies are classified according to whether tau deposits predominantly contain tau
isoforms with three or four repeats of the microtubule-binding domain. Those in which four …

Redefining the multidimensional clinical phenotypes of frontotemporal lobar degeneration syndromes

AG Murley, I Coyle-Gilchrist, MA Rouse, PS Jones, W Li… - Brain, 2020 - academic.oup.com
The syndromes caused by frontotemporal lobar degeneration have highly heterogeneous
and overlap** clinical features. There has been great progress in the refinement of clinical …

Radiological biomarkers for diagnosis in PSP: where are we and where do we need to be?

JL Whitwell, GU Höglinger, A Antonini… - Movement …, 2017 - Wiley Online Library
ABSTRACT PSP is a pathologically defined neurodegenerative tauopathy with a variety of
clinical presentations including typical Richardson's syndrome and other variant PSP …

Sensitivity and specificity of diagnostic criteria for progressive supranuclear palsy

F Ali, PR Martin, H Botha, JE Ahlskog… - Movement …, 2019 - Wiley Online Library
Abstract Background In 2017, the International Parkinson and Movement Disorder Society
put forward new clinical criteria for the diagnosis of PSP, recognizing diverse PSP …

Clinical, anatomical, and pathological features in the three variants of primary progressive aphasia: a review

M Montembeault, SM Brambati… - Frontiers in …, 2018 - frontiersin.org
Primary progressive aphasias (PPA) are neurodegenerative diseases clinically
characterized by an early and relatively isolated language impairment. Three main clinical …

A molecular pathology, neurobiology, biochemical, genetic and neuroimaging study of progressive apraxia of speech

KA Josephs, JR Duffy, HM Clark, RL Utianski… - Nature …, 2021 - nature.com
Progressive apraxia of speech is a neurodegenerative syndrome affecting spoken
communication. Molecular pathology, biochemistry, genetics, and longitudinal imaging were …

Primary progressive apraxia of speech: From recognition to diagnosis and care

JR Duffy, RL Utianski, KA Josephs - Aphasiology, 2021 - Taylor & Francis
Background Apraxia of speech (AOS) can be caused by neurodegenerative disease and
sometimes is its presenting sign (ie, primary progressive apraxia of speech, PPAOS). During …

Retraining speech production and fluency in non-fluent/agrammatic primary progressive aphasia

ML Henry, HI Hubbard, SM Grasso, ML Mandelli… - Brain, 2018 - academic.oup.com
The non-fluent/agrammatic variant of primary progressive aphasia (nfvPPA) presents with a
gradual decline in grammar and motor speech resulting from selective degeneration of …

[HTML][HTML] Neuroimaging in frontotemporal dementia: heterogeneity and relationships with underlying neuropathology

BT Peet, S Spina, N Mundada, R La Joie - Neurotherapeutics, 2021 - Elsevier
Frontotemporal dementia encompasses a group of clinical syndromes defined
pathologically by degeneration of the frontal and temporal lobes. Historically, these …