Targeting biomolecular condensation and protein aggregation against cancer

JL Silva, D Foguel, VF Ferreira, TCRG Vieira… - Chemical …, 2023 - ACS Publications
Biomolecular condensates, membrane-less entities arising from liquid–liquid phase
separation, hold dichotomous roles in health and disease. Alongside their physiological …

Physiological functions of the cellular prion protein

AR Castle, AC Gill - Frontiers in molecular biosciences, 2017 - frontiersin.org
The prion protein, PrPC, is a small, cell-surface glycoprotein notable primarily for its critical
role in pathogenesis of the neurodegenerative disorders known as prion diseases. A …

Physiology of the prion protein

R Linden, VR Martins, MAM Prado… - Physiological …, 2008 - journals.physiology.org
Prion diseases are transmissible spongiform encephalopathies (TSEs), attributed to
conformational conversion of the cellular prion protein (PrPC) into an abnormal conformer …

[HTML][HTML] The cellular prion protein (PrPC): its physiological function and role in disease

L Westergard, HM Christensen, DA Harris - Biochimica et Biophysica Acta …, 2007 - Elsevier
Prion diseases are caused by conversion of a normal cell-surface glycoprotein (PrPC) into a
conformationally altered isoform (PrPSc) that is infectious in the absence of nucleic acid …

p53 in neuronal apoptosis

C Culmsee, MP Mattson - Biochemical and biophysical research …, 2005 - Elsevier
The tumor suppressor and transcription factor p53 is a key modulator of cellular stress
responses, and activation of p53 can trigger apoptosis in many cell types including neurons …

Presenilin-dependent transcriptional control of the Aβ-degrading enzyme neprilysin by intracellular domains of βAPP and APLP

R Pardossi-Piquard, A Petit, T Kawarai, C Sunyach… - Neuron, 2005 - cell.com
Amyloid β-peptide (Aβ), which plays a central role in Alzheimer's disease, is generated by
presenilin-dependent γ-secretase cleavage of β-amyloid precursor protein (βAPP). We …

Activated protein C prevents neuronal apoptosis via protease activated receptors 1 and 3

H Guo, D Liu, H Gelbard, T Cheng, R Insalaco… - Neuron, 2004 - cell.com
Activated protein C (APC), a serine protease with anticoagulant and anti-inflammatory
activities, exerts direct cytoprotective effects on endothelium via endothelial protein C …

Lethal recessive myelin toxicity of prion protein lacking its central domain

F Baumann, M Tolnay, C Brabeck, J Pahnke… - The EMBO …, 2007 - embopress.org
PrPC‐deficient mice expressing prion protein variants with large amino‐proximal deletions
(termed PrPΔF) suffer from neurodegeneration, which is rescued by full‐length PrPC. We …

The function of the cellular prion protein in health and disease

JC Watts, MEC Bourkas, H Arshad - Acta neuropathologica, 2018 - Springer
The essential role of the cellular prion protein (PrP C) in prion disorders such as Creutzfeldt–
Jakob disease is well documented. Moreover, evidence is accumulating that PrP C may act …

The α-secretase-derived N-terminal product of cellular prion, N1, displays neuroprotective function in vitro and in vivo

MV Guillot-Sestier, C Sunyach, C Druon… - Journal of Biological …, 2009 - ASBMB
Cellular prion protein (PrP c) undergoes a disintegrin-mediated physiological cleavage,
generating a soluble amino-terminal fragment (N1), the function of which remained …