Huntington disease: natural history, biomarkers and prospects for therapeutics

CA Ross, EH Aylward, EJ Wild, DR Langbehn… - Nature Reviews …, 2014 - nature.com
Huntington disease (HD) can be seen as a model neurodegenerative disorder, in that it is
caused by a single genetic mutation and is amenable to predictive genetic testing, with …

Voxel-based morphometry of the human brain: methods and applications

A Mechelli, CJ Price, KJ Friston… - Current Medical …, 2005 - ingentaconnect.com
In recent years, a whole-brain unbiased objective technique, known as voxel-based
morphometry (VBM), has been developed to characterise brain differences in vivo using …

Biological and clinical manifestations of Huntington's disease in the longitudinal TRACK-HD study: cross-sectional analysis of baseline data

SJ Tabrizi, DR Langbehn, BR Leavitt… - The Lancet …, 2009 - thelancet.com
Background Huntington's disease (HD) is an autosomal dominant, fully penetrant,
neurodegenerative disease that most commonly affects adults in mid-life. Our aim was to …

Detection of Huntington's disease decades before diagnosis: the Predict-HD study

JS Paulsen, DR Langbehn, JC Stout… - Journal of Neurology …, 2008 - jnnp.bmj.com
Objective: The objective of the Predict-HD study is to use genetic, neurobiological and
refined clinical markers to understand the early progression of Huntington's disease (HD) …

Biological and clinical changes in premanifest and early stage Huntington's disease in the TRACK-HD study: the 12-month longitudinal analysis

SJ Tabrizi, RI Scahill, A Durr, RAC Roos… - The Lancet …, 2011 - thelancet.com
Background TRACK-HD is a prospective observational study of Huntington's disease (HD)
that examines disease progression in premanifest individuals carrying the mutant HTT gene …

The cognitive neuroscience of response inhibition: relevance for genetic research in attention-deficit/hyperactivity disorder

AR Aron, RA Poldrack - Biological psychiatry, 2005 - Elsevier
Psychological functions that are behaviorally and neurally well specified may serve as
endophenotypes for attention-deficit/hyperactivity disorder (ADHD) research. Such …

MRI-derived measurements of human subcortical, ventricular and intracranial brain volumes: reliability effects of scan sessions, acquisition sequences, data analyses …

J Jovicich, S Czanner, X Han, D Salat… - Neuroimage, 2009 - Elsevier
Automated MRI-derived measurements of in-vivo human brain volumes provide novel
insights into normal and abnormal neuroanatomy, but little is known about measurement …

Where in the brain is depression?

M Pandya, M Altinay, DA Malone, A Anand - Current psychiatry reports, 2012 - Springer
Major depressive disorder is a serious medical illness which is responsible for considerable
morbidity and disability. Despite decades of research, the neural basis for depression is still …

Stem cell‐based cell therapy in neurological diseases: a review

SU Kim, J De Vellis - Journal of neuroscience research, 2009 - Wiley Online Library
Human neurological disorders such as Parkinson's disease, Huntington's disease,
amyotrophic lateral sclerosis (ALS), Alzheimer's disease, multiple sclerosis (MS), stroke, and …

Cerebral cortex and the clinical expression of Huntington's disease: complexity and heterogeneity

HD Rosas, DH Salat, SY Lee, AK Zaleta, V Pappu… - Brain, 2008 - academic.oup.com
The clinical phenotype of Huntington's disease (HD) is far more complex and variable than
depictions of it as a progressive movement disorder dominated by neostriatal pathology …