Dopamine transporter deficiency syndrome (DTDS): expanding the clinical phenotype and precision medicine approaches

J Ng, S Barral, SN Waddington, MA Kurian - Cells, 2023 - mdpi.com
Infantile parkinsonism-dystonia due to dopamine transporter deficiency syndrome (DTDS) is
an ultrarare childhood movement disorder caused by biallelic loss-of-function mutations in …

Genomic investigations of unexplained acute hepatitis in children

S Morfopoulou, S Buddle, OE Torres Montaguth… - Nature, 2023 - nature.com
Since its first identification in Scotland, over 1,000 cases of unexplained paediatric hepatitis
in children have been reported worldwide, including 278 cases in the UK. Here we report an …

A transporter's doom or destiny: SLC6A1 in health and disease, novel molecular targets and emerging therapeutic prospects

N Shah, AS Kasture, FP Fischer, HH Sitte… - Frontiers in Molecular …, 2024 - frontiersin.org
As the first member of the solute carrier 6 (SLC6) protein family, the γ-aminobutyric acid
(GABA) transporter 1 (GAT1, SLC6A1), plays a pivotal role in the uptake of GABA from the …

On-demand cell-autonomous gene therapy for brain circuit disorders

Y Qiu, N O'Neill, B Maffei, C Zourray… - Science, 2022 - science.org
Several neurodevelopmental and neuropsychiatric disorders are characterized by
intermittent episodes of pathological activity. Although genetic therapies offer the ability to …

Gene therapy for neurotransmitter‐related disorders

WS Chu, J Ng, SN Waddington… - Journal of Inherited …, 2024 - Wiley Online Library
Inborn errors of neurotransmitter (NT) metabolism are a group of rare, heterogenous
diseases with predominant neurological features, such as movement disorders, autonomic …

Virus-inspired nanosystems for drug delivery

Z Liao, L Tu, X Li, XJ Liang, S Huo - Nanoscale, 2021 - pubs.rsc.org
With over millions of years of evolution, viruses can infect cells efficiently by utilizing their
unique structures. Similarly, the drug delivery process is designed to imitate the viral …

Molecular and clinical repercussions of GABA transporter 1 variants gone amiss: links to epilepsy and developmental spectrum disorders

FP Fischer, AS Kasture, T Hummel… - Frontiers in molecular …, 2022 - frontiersin.org
The human γ-aminobutyric acid (GABA) transporter 1 (hGAT-1) is the first member of the
solute carrier 6 (SLC6) protein superfamily. GAT-1 (SLC6A1) is one of the main GABA …

Engineered stem cells by emerging biomedical stratagems

J Wang, X Zhang, H Chen, H Ren, M Zhou, Y Zhao - Science Bulletin, 2024 - Elsevier
Stem cell therapy holds immense potential as a viable treatment for a widespread range of
intractable disorders. As the safety of stem cell transplantation having been demonstrated in …

Mouse models for inherited monoamine neurotransmitter disorders

B Thöny, J Ng, MA Kurian, P Mills… - Journal of Inherited …, 2024 - Wiley Online Library
Several mouse models have been developed to study human defects of primary and
secondary inherited monoamine neurotransmitter disorders (iMND). As the field continues to …

Gene replacement therapies for inherited disorders of neurotransmission: Current progress in succinic semialdehyde dehydrogenase deficiency

HHC Lee, IT Latzer, M Bertoldi, G Gao… - Journal of Inherited …, 2024 - Wiley Online Library
Neurodevelopment is a highly organized and complex process involving lasting and often
irreversible changes in the central nervous system. Inherited disorders of neurotransmission …