BRCAness revisited

CJ Lord, A Ashworth - Nature Reviews Cancer, 2016 - nature.com
Over the past 20 years, there has been considerable progress in our understanding of the
biological functions of the BRCA1 and BRCA2 cancer susceptibility genes. This has led to …

Ewing sarcoma—diagnosis, treatment, clinical challenges and future perspectives

SK Zöllner, JF Amatruda, S Bauer, S Collaud… - Journal of clinical …, 2021 - mdpi.com
Ewing sarcoma, a highly aggressive bone and soft-tissue cancer, is considered a prime
example of the paradigms of a translocation-positive sarcoma: a genetically rather simple …

Ewing's sarcoma

N Riggi, ML Suvà, I Stamenkovic - New England Journal of …, 2021 - Mass Medical Soc
Ewing's Sarcoma Ewing's sarcoma, an aggressive cancer of bone and soft tissue, primarily
affects children and young adults. A t (11; 22) translocation is noted in 85 to 90% of cases …

The ETS family of oncogenic transcription factors in solid tumours

GM Sizemore, JR Pitarresi, S Balakrishnan… - Nature Reviews …, 2017 - nature.com
Findings over the past decade have identified aberrant activation of the ETS transcription
factor family throughout all stages of tumorigenesis. Specifically in solid tumours, gene …

An update on poly (ADP-ribose) polymerase-1 (PARP-1) inhibitors: opportunities and challenges in cancer therapy

YQ Wang, PY Wang, YT Wang, GF Yang… - Journal of medicinal …, 2016 - ACS Publications
Poly (ADP-ribose) polymerase-1 (PARP-1) is a critical DNA repair enzyme in the base
excision repair pathway. Inhibitors of this enzyme comprise a new type of anticancer drug …

EWS/FLI confers tumor cell synthetic lethality to CDK12 inhibition in Ewing sarcoma

AB Iniguez, B Stolte, EJ Wang, AS Conway, G Alexe… - Cancer cell, 2018 - cell.com
Many cancer types are driven by oncogenic transcription factors that have been difficult to
drug. Transcriptional inhibitors, however, may offer inroads into targeting these cancers …

Biology of bone sarcomas and new therapeutic developments

HK Brown, K Schiavone, F Gouin, MF Heymann… - Calcified tissue …, 2018 - Springer
Bone sarcomas are tumours belonging to the family of mesenchymal tumours and constitute
a highly heterogeneous tumour group. The three main bone sarcomas are osteosarcoma …

A review of soft-tissue sarcomas: translation of biological advances into treatment measures

NT Hoang, LA Acevedo, MJ Mann… - Cancer management and …, 2018 - Taylor & Francis
Soft-tissue sarcomas are rare malignant tumors arising from connective tissues and have an
overall incidence of about five per 100,000 per year. While this diverse family of …

PARP inhibitor combination therapy

A Drean, CJ Lord, A Ashworth - Critical reviews in oncology/hematology, 2016 - Elsevier
Abstract In 2014, olaparib (Lynparza) became the first PARP (Poly (ADP-ribose)
polymerase) inhibitor to be approved for the treatment of cancer. When used as single …

Olaparib: first global approval

ED Deeks - Drugs, 2015 - Springer
Olaparib (Lynparza™) is an oral, small molecule, poly (ADP-ribose) polymerase inhibitor
being developed by AstraZeneca for the treatment of solid tumours. The primary indication …