Fuchs endothelial corneal dystrophy: The vicious cycle of Fuchs pathogenesis

SO Tone, V Kocaba, M Böhm, A Wylegala… - Progress in Retinal and …, 2021 - Elsevier
Fuchs endothelial corneal dystrophy (FECD) is the most common primary corneal
endothelial dystrophy and the leading indication for corneal transplantation worldwide …

Oxidative stress and reactive oxygen species: a review of their role in ocular disease

L Ung, U Pattamatta, N Carnt… - Clinical …, 2017 - portlandpress.com
For many years, oxidative stress arising from the ubiquitous production of reactive oxygen
species (ROS) has been implicated in the pathogenesis of various eye diseases. While …

[HTML][HTML] Current understanding of the pathogenesis of Fuchs' endothelial corneal dystrophy

GG Nanda, DP Alone - Molecular vision, 2019 - ncbi.nlm.nih.gov
Fuchs' endothelial corneal dystrophy (FECD) is the most prominent reason for corneal-
endothelial transplantations across the globe. The disease pathophysiology manifests …

Diseases of the corneal endothelium

LJ Jeang, CE Margo, EM Espana - Experimental eye research, 2021 - Elsevier
The corneal endothelial monolayer and associated Descemet's membrane (DM) complex is
a unique structure that plays an essential role in corneal function. Endothelial cells are …

Feeder-free differentiation of cells exhibiting characteristics of corneal endothelium from human induced pluripotent stem cells

MD Wagoner, LR Bohrer, BT Aldrich… - Biology …, 2018 - journals.biologists.com
The purpose of this study was to devise a strategy for the derivation of corneal endothelial
cells (CEnCs) from adult fibroblast-derived induced pluripotent stem cells (iPSCs). IPSCs …

[HTML][HTML] Mitochondrial ROS induced lysosomal dysfunction and autophagy impairment in an animal model of congenital hereditary endothelial dystrophy

R Shyam, DG Ogando, M Choi, PB Liton… - … & Visual Science, 2021 - jov.arvojournals.org
Purpose: The Slc4a11 knock out (KO) mouse model recapitulates the human disease
phenotype associated with congenital hereditary endothelial dystrophy (CHED). Increased …

Potential theranostic roles of SLC4 molecules in human diseases

J Zhong, J Dong, W Ruan, X Duan - International Journal of Molecular …, 2023 - mdpi.com
The solute carrier family 4 (SLC4) is an important protein responsible for the transport of
various ions across the cell membrane and mediating diverse physiological functions, such …

The H+ Transporter SLC4A11: Roles in Metabolism, Oxidative Stress and Mitochondrial Uncoupling

JA Bonanno, R Shyam, M Choi, DG Ogando - Cells, 2022 - mdpi.com
Solute-linked cotransporter, SLC4A11, a member of the bicarbonate transporter family, is an
electrogenic H+ transporter activated by NH3 and alkaline pH. Although SLC4A11 does not …

[HTML][HTML] Ammonia sensitive SLC4A11 mitochondrial uncoupling reduces glutamine induced oxidative stress

DG Ogando, M Choi, R Shyam, S Li, JA Bonanno - Redox biology, 2019 - Elsevier
Abstract SLC4A11 is a NH 3 sensitive membrane transporter with H+ channel-like properties
that facilitates Glutamine catabolism in Human and Mouse corneal endothelium (CE). Loss …

The molecular basis of fuchs' endothelial corneal dystrophy

J Zhang, CNJ McGhee, DV Patel - Molecular diagnosis & therapy, 2019 - Springer
Fuchs' endothelial corneal dystrophy (FECD) is a common disease resulting from corneal
endothelial cell dysfunction. It is inherited in an autosomal dominant fashion with incomplete …