[HTML][HTML] Li-fraumeni syndrome

K Schneider, K Zelley, KE Nichols… - GeneReviews® …, 2024 - ncbi.nlm.nih.gov
Li-Fraumeni syndrome (LFS) is a cancer predisposition syndrome associated with high risks
for a broad spectrum of cancers including early-onset cancers. Five cancer types account for …

Clonal hematopoiesis, inflammation, and hematologic malignancy

R Kanagal-Shamanna, DB Beck… - Annual Review of …, 2024 - annualreviews.org
Somatic or acquired mutations are postzygotic genetic variations that can occur within any
tissue. These mutations accumulate during aging and have classically been linked to …

Recommendations for reporting of secondary findings in clinical exome and genome sequencing, 2021 update: a policy statement of the American College of Medical …

DT Miller, K Lee, AS Gordon, LM Amendola… - Genetics in …, 2021 - nature.com
Disclaimer: This statement is designed primarily as an educational resource for medical
geneticists and other clinicians to help them provide quality medical services. Adherence to …

Specifications of the ACMG/AMP variant interpretation guidelines for germline TP53 variants

C Fortuno, K Lee, M Olivier, T Pesaran, PL Mai… - Human …, 2021 - Wiley Online Library
Germline pathogenic variants in TP53 are associated with Li‐Fraumeni syndrome, a cancer
predisposition disorder inherited in an autosomal dominant pattern associated with a high …

Differences in cancer phenotypes among frequent CHEK2 variants and implications for clinical care—checking CHEK2

BL Bychkovsky, NB Agaoglu, C Horton, J Zhou… - Jama …, 2022 - jamanetwork.com
Importance GermlineCHEK2pathogenic variants (PVs) are frequently detected by multigene
cancer panel testing (MGPT), but our understanding of PVs beyond c. 1100del has been …

[HTML][HTML] Germline TP53 pathogenic variants and breast cancer: A narrative review

E Blondeaux, L Arecco, K Punie, R Graffeo… - Cancer treatment …, 2023 - Elsevier
Approximately 10% of breast cancers are associated with the inheritance of a pathogenic
variant (PV) in one of the breast cancer susceptibility genes. Multiple breast cancer …

Clinical and therapeutic implications of clonal hematopoiesis

G Petrone, I Turker, P Natarajan… - Annual Review of …, 2024 - annualreviews.org
Clonal hematopoiesis (CH) is an age-related process whereby hematopoietic stem and
progenitor cells (HSPCs) acquire mutations that lead to a proliferative advantage and clonal …

Aligning germline cancer predisposition with tumor-based next-generation sequencing for modern oncology diagnosis, interception, and therapeutic development

TA Yap, ZK Stadler, LA Stout… - American Society of …, 2023 - ascopubs.org
In the era of precision medicine, genomic interrogation for identification of both germline and
somatic genetic alterations has become increasingly important. While such germline testing …

[HTML][HTML] Clonal hematopoiesis in cancer

SJ Park, R Bejar - Experimental hematology, 2020 - Elsevier
Highlights•The clinical implications of clonal hematopoiesis in the cancer setting are
reviewed.•The biologic interplay between clonal hematopoiesis and development of solid …

Preclinical models of adrenocortical cancer

AJH Sedlack, SJ Hatfield, S Kumar, Y Arakawa… - Cancers, 2023 - mdpi.com
Simple Summary Adrenocortical cancer is a very rare form of endocrine cancer with dismal
prognosis. Preclinical models such as cell lines, organoids, and mouse models are essential …