Fibrinogen and fibrin: synthesis, structure, and function in health and disease

AS Wolberg - Journal of Thrombosis and Haemostasis, 2023‏ - Elsevier
Fibrinogen is an extraordinary molecule by any estimation. It is large, structurally intricate,
and circulates at high concentrations. Its biological end product, insoluble fibrin (ogen) or …

Fibrin clot structure and function: a role in the pathophysiology of arterial and venous thromboembolic diseases

A Undas, RAS Ariëns - Arteriosclerosis, thrombosis, and vascular …, 2011‏ - ahajournals.org
The formation of fibrin clots that are relatively resistant to lysis represents the final step in
blood coagulation. We discuss the genetic and environmental regulators of fibrin structure in …

Factor XIII: a coagulation factor with multiple plasmatic and cellular functions

L Muszbek, Z Bereczky, Z Bagoly… - Physiological …, 2011‏ - journals.physiology.org
Factor XIII (FXIII) is unique among clotting factors for a number of reasons: 1) it is a
protransglutaminase, which becomes activated in the last stage of coagulation; 2) it works …

Fibrinogen and factor XIII in venous thrombosis and thrombus stability

AS Wolberg, Y Sang - Arteriosclerosis, thrombosis, and vascular …, 2022‏ - ahajournals.org
As the third most common vascular disease, venous thromboembolism is associated with
significant mortality and morbidity. Pathogenesis underlying venous thrombosis is still not …

Structure of fibrin: impact on clot stability

JW Weisel - Journal of Thrombosis and Haemostasis, 2007‏ - Wiley Online Library
Information on the structural origins of clot stability is necessary for understanding the
functions and pathology of fibrin clots and thrombi, but is also important for interpreting …

Directing thrombin

DA Lane, H Philippou, JA Huntington - Blood, 2005‏ - ashpublications.org
Following initiation of coagulation as part of the hemostatic response to injury, thrombin is
generated from its inactive precursor prothrombin by factor Xa as part of the prothrombinase …

Factor XIII activity mediates red blood cell retention in venous thrombi

MM Aleman, JR Byrnes, JG Wang, R Tran… - The Journal of clinical …, 2014‏ - jci.org
Venous thrombi, fibrin-and rbc-rich clots triggered by inflammation and blood stasis, underlie
devastating, and sometimes fatal, occlusive events. During intravascular fibrin deposition …

Transglutaminases and disease: lessons from genetically engineered mouse models and inherited disorders

SE Iismaa, BM Mearns, L Lorand… - Physiological …, 2009‏ - journals.physiology.org
The human transglutaminase (TG) family consists of a structural protein, protein 4.2, that
lacks catalytic activity, and eight zymogens/enzymes, designated factor XIII-A (FXIII-A) and …

Role of factor XIII in fibrin clot formation and effects of genetic polymorphisms

RAS Ariëns, TS Lai, JW Weisel… - Blood, The Journal …, 2002‏ - ashpublications.org
Factor XIII and fibrinogen are unusual among clotting factors in that neither is a serine
protease. Fibrin is the main protein constituent of the blood clot, which is stabilized by factor …

Genetic risk factors of venous thrombosis

RF Franco, PH Reitsma - Human genetics, 2001‏ - Springer
Venous thrombosis, whose main clinical presentations include deep vein thrombosis and
pulmonary embolism, represents a major health problem worldwide. Numerous conditions …