Deciphering the tubulin language: Molecular determinants and readout mechanisms of the tubulin code in neurons

R Zocchi, C Compagnucci, E Bertini… - International Journal of …, 2023‏ - mdpi.com
Microtubules (MTs) are dynamic components of the cell cytoskeleton involved in several
cellular functions, such as structural support, migration and intracellular trafficking. Despite …

Dystonia genes and their biological pathways

A Di Fonzo, HA **nah, M Zech - International review of neurobiology, 2023‏ - Elsevier
High-throughput sequencing has been instrumental in uncovering the spectrum of
pathogenic genetic alterations that contribute to the etiology of dystonia. Despite the …

Monogenic disorders associated with motor speech phenotypes in children and adolescents undergoing clinical exome sequencing

MW Mitchel, M Oetjens, ASF Berry, A Johns… - Genetics in …, 2025‏ - Elsevier
Purpose Prior studies investigating the genetic architecture of pediatric motor speech
disorders (MSDs) have been limited by small sample sizes and an exclusive focus on …

Hypomyelinating leukodystrophy and movement disorders

J Ganguly, J Sinha, P Basu, A Pal… - Annals of Movement …, 2023‏ - journals.lww.com
Hypomyelinating leukodystrophies (HLDs) are a heterogeneous group of disorders caused
by primary deficit in myelin development; they are radiologically characterized by mild T2 …

Developmental regression with early feeding difficulties and characteristic neuroimaging features of H‐ABC in an infant from a TUBB4A genetic variant.

B Charles‐Britton, YL Leong, D Clark… - … of Paediatrics & …, 2023‏ - search.ebscohost.com
This article discusses a case report of an infant with developmental regression and early
feeding difficulties, which were found to be caused by a genetic variant in the TUBB4A gene …

Expanding the phenotypic and genotypic spectrum of DYT-TUBB4A with seven patients from India

D Garg, VV Holla, J Ganguly, R Rajan, A Saini… - Parkinsonism & Related …, 2024‏ - Elsevier
Background Variants in the TUBB4A gene are associated with dystonia (DYT-TUBB4A),
Hypomyelination with Atrophy of the Basal Ganglia and Cerebellum (H-ABC) and spastic …

[HTML][HTML] Genetic Diversity and Expanded Phenotypes in Dystonia: Insights from Large-Scale Exome Sequencing

M Thomsen, F Ott, S Loens, G Kilic-Berkmen… - medRxiv, 2024‏ - pmc.ncbi.nlm.nih.gov
Dystonia is one of the most prevalent movement disorders, characterized by significant
clinical and etiological heterogeneity. Despite considerable heritability (∼ 25%) and the …

DYT-TUBB4A: first family from India with the Arg2Gly mutation

D Garg, V Aggarwal - Annals of Indian Academy of Neurology, 2023‏ - journals.lww.com
DYT‑TUBB4A, formerly known as DYT‑4, was first reported by Parker et al. in 1985,[1] and
was termed 'whispering dysphonia'due to laryngeal dystonia. It occurs due to mutations in …

Isolated and combined dystonias: Update

N Bukhari-Parlakturk, SJ Frucht - Handbook of Clinical Neurology, 2023‏ - Elsevier
Dystonia is a hyperkinetic movement disorder with a unique motor phenomenology that can
manifest as an isolated clinical syndrome or combined with other neurological features. This …

Exploring next generation sequencing in the diagnosis of inherited ataxia and other neurological diseases

J Hersheson - 2024‏ - discovery.ucl.ac.uk
Neurodegenerative diseases are a complex and heterogeneous group of disorders
characterised by progressive loss of cells from the central nervous system which can result …