Novel hereditary angioedema linked with a heparan sulfate 3-O-sulfotransferase 6 gene mutation

K Bork, K Wulff, BS Möhl, L Steinmüller-Magin… - Journal of Allergy and …, 2021 - Elsevier
Background Hereditary angioedema (HAE) is a potentially fatal disorder resulting in
recurrent attacks of severe swelling. It may be associated with a genetic deficiency of …

The rebirth of the contact pathway: a new therapeutic target

P Srivastava, D Gailani - Current opinion in hematology, 2020 - journals.lww.com
The rebirth of the contact pathway: a new therapeutic target : Current Opinion in Hematology
The rebirth of the contact pathway: a new therapeutic target : Current Opinion in Hematology …

Exploring bradykinin: A common mediator in the pathophysiology of sepsis and atherosclerotic cardiovascular disease

MZ Siti-Zubaidah, HS Harafinova, AN Liba… - Vascular …, 2024 - Elsevier
Sepsis and atherosclerotic cardiovascular disease (ASCVD) are major health challenges
involving complex processes like inflammation, renin-angiotensin system (RAS) …

[HTML][HTML] First randomized evaluation of safety, pharmacodynamics, and pharmacokinetics of BAY 1831865, an antibody targeting coagulation factor XI and factor XIa …

B Nowotny, D Thomas, S Schwers, S Wiegmann… - Journal of Thrombosis …, 2022 - Elsevier
Background Bleeding is a clinically significant issue with all current anticoagulants. Safer
antithrombotic strategies are required. Objectives To investigate the safety …

[HTML][HTML] The contact pathway and sepsis

V Raghunathan, J Zilberman‐Rudenko… - Research and Practice …, 2019 - Elsevier
The contact pathway factors XI (FXI) and XII (FXII) have been demonstrated to be largely
dispensable for hemostasis, as their absence results in a mild to absent bleeding diathesis …

Substrates, cofactors, and cellular targets of coagulation factor XIa

AL Lira, TCL Kohs, SA Moellmer… - … in thrombosis and …, 2023 - thieme-connect.com
Coagulation factor XI (FXI) has increasingly been shown to play an integral role in several
physiologic and pathological processes. FXI is among several zymogens within the blood …

Factor XII and kininogen asymmetric assembly with gC1qR/C1QBP/P32 is governed by allostery

BG Kaira, A Slater, KR McCrae… - Blood, The Journal …, 2020 - ashpublications.org
The contact system is composed of factor XII (FXII), prekallikrein (PK), and cofactor high-
molecular-weight kininogen (HK). The globular C1q receptor (gC1qR) has been shown to …

[HTML][HTML] Plasma kallikrein structure reveals apple domain disc rotated conformation compared to factor XI

C Li, KM Voos, M Pathak, G Hall, KR McCrae… - Journal of Thrombosis …, 2019 - Elsevier
Essentials• Zymogen PK is activated to PKa and cleaves substrates kininogen and FXII
contributing to bradykinin generation.• Monomeric PKa and dimeric homologue FXI utilize …

Penicillin causes non-allergic anaphylaxis by activating the contact system

Y Gao, Y Han, X Zhang, Q Fei, R Qi, R Hou, R Cai… - Scientific reports, 2020 - nature.com
Immediate hypersensitivity reaction (IHR) can be divided into allergic-and non-allergic-
mediated, while “anaphylaxis” is reserved for severe IHR. Clinically, true penicillin allergy is …

A Model of Zymogen Factor XII: Insights into Protease Activation

A Shamanaev, Y Ma, MB Ponczek, M Sun… - Blood …, 2025 - ashpublications.org
In plasma, the zymogens factor XII (FXII) and prekallikrein reciprocally convert each other to
the proteases FXIIa and plasma kallikrein (PKa). PKa cleaves high-molecular-weight …