Congenital long QT syndrome

AD Krahn, Z Laksman, RW Sy, PG Postema… - Clinical …, 2022 - jacc.org
Congenital long QT syndrome (LQTS) encompasses a group of heritable conditions that are
associated with cardiac repolarization dysfunction. Since its initial description in 1957, our …

Provocation testing in congenital long QT syndrome: a practical guide

T Abrahams, B Davies, Z Laksman, RW Sy… - Heart rhythm, 2023 - Elsevier
Congenital long QT syndrome (LQTS) is a hereditary cardiac channelopathy with an
estimated prevalence of 1 in 2500. A prolonged resting QT interval corrected for heart rate …

Diagnostic Accuracy of the Standing Test in Adults Suspected for Congenital Long‐QT Syndrome

AS Vink, BJM Hermans, JLQ Hooglugt… - Journal of the …, 2023 - ahajournals.org
Background An elegant bedside provocation test has been shown to aid the diagnosis of
long‐QT syndrome (LQTS) in a retrospective cohort by evaluation of QT intervals and T …

Utility of Provocative Testing in the Diagnosis and Genoty** of Congenital Long QT Syndrome: A Systematic Review and Meta‐Analysis

Y Yang, T Lv, S Li, P Liu, Q Gao… - Journal of the American …, 2022 - ahajournals.org
Background Diagnosis is particularly challenging in concealed or asymptomatic long QT
syndrome (LQTS). Provocative testing, unmasking the characterization of LQTS, is a …

Proceed with caution: Standard protocol exercise stress tests fail to replicate the diagnostic utility of supine‐stand tests for long QT syndrome

AM Pinsky, VK Kulkarni, JM Bos… - Pacing and Clinical …, 2024 - Wiley Online Library
Abstract Background Long QT syndrome (LQTS) is a sudden death predisposing condition
characterized by ECG‐derived prolongation of the QT interval. Previous studies have …

QT interval in children with orthostatic dysregulation: Changes in standing load

M Sakata, Y Oyazato, A Nishiyama - Pediatrics International, 2024 - Wiley Online Library
Background The corrected QT interval (QTc) is affected by changes in autonomic
sympathovagal modulation. The aim of this study was to determine whether children with …

先天性 QT 延長症候群の診療

小澤淳一, 鈴木博 - Pediatric Cardiology and Cardiac Surgery, 2024 - jpccs.jp
Pediatric Cardiology and Cardiac Surgery 40(3): 151-162 (2024) ロゴ 日本小児循環器学会雑誌
Pediatric Cardiology and Cardiac Surgery Online ISSN: 2187-2988 Print ISSN: 0911-1794 特定 …

Valutazione del QTc prima e dopo test da sforzo in una popolazione di pazienti affetti da obesità severa: possibile associazione con l'apnea ostruttiva nel sonno

M CASARIN - thesis.unipd.it
Obesity is associated with QT interval prolongation. Obesity is also associated with OSA
(obstructive sleep apnoea). OSA as well is associated with prolongation of the QT interval …