Mechanisms of autoantibody-induced pathology

RJ Ludwig, K Vanhoorelbeke, F Leypoldt… - Frontiers in …, 2017‏ - frontiersin.org
Autoantibodies are frequently observed in healthy individuals. In a minority of these
individuals, they lead to manifestation of autoimmune diseases, such as rheumatoid arthritis …

Thrombotic thrombocytopenic purpura

JA Kremer Hovinga, P Coppo, B Lämmle… - Nature reviews Disease …, 2017‏ - nature.com
Thrombotic thrombocytopenic purpura (TTP; also known as Moschcowitz disease) is
characterized by the concomitant occurrence of often severe thrombocytopenia …

An international consensus approach to the management of atypical hemolytic uremic syndrome in children

C Loirat, F Fakhouri, G Ariceta, N Besbas, M Bitzan… - Pediatric …, 2016‏ - Springer
Atypical hemolytic uremic syndrome (aHUS) emerged during the last decade as a disease
largely of complement dysregulation. This advance facilitated the development of novel …

HUS and atypical HUS

TS Jokiranta - Blood, The Journal of the American Society of …, 2017‏ - ashpublications.org
Hemolytic uremic syndrome (HUS) is a thrombotic microangiopathy characterized by
intravascular hemolysis, thrombocytopenia, and acute kidney failure. HUS is usually …

STEC-HUS, atypical HUS and TTP are all diseases of complement activation

M Noris, F Mescia, G Remuzzi - Nature Reviews Nephrology, 2012‏ - nature.com
Haemolytic uraemic syndrome (HUS) and thrombotic thrombocytopaenic purpura (TTP) are
diseases characterized by microvascular thrombosis, with consequent thrombocytopaenia …

Use of eculizumab for atypical haemolytic uraemic syndrome and C3 glomerulopathies

J Zuber, F Fakhouri, LT Roumenina, C Loirat… - Nature Reviews …, 2012‏ - nature.com
In the past decade, a large body of evidence has accumulated in support of the critical role
of dysregulation of the alternative complement pathway in atypical haemolytic uraemic …

How I treat refractory thrombotic thrombocytopenic purpura

FA Sayani, CS Abrams - Blood, The Journal of the American …, 2015‏ - ashpublications.org
Acquired thrombotic thrombocytopenic purpura (TTP) is characterized by thrombocytopenia
and microangiopathic hemolytic anemia (MAHA) without an obvious cause, and may include …

Brain histopathology in patients with systemic lupus erythematosus: identification of lesions associated with clinical neuropsychiatric lupus syndromes and the role of …

D Cohen, EC Rijnink, RJA Nabuurs… - …, 2016‏ - academic.oup.com
Objectives. Neuropsychiatric (NP) involvement is a poorly understood manifestation of SLE.
We studied post-mortem histopathology in relation to clinical NPSLE syndromes and …

Update on hemolytic uremic syndrome: Diagnostic and therapeutic recommendations

M Salvadori, E Bertoni - World journal of nephrology, 2013‏ - pmc.ncbi.nlm.nih.gov
Hemolytic uremic syndrome (HUS) is a rare disease. In this work the authors review the
recent findings on HUS, considering the different etiologic and pathogenetic classifications …

Spectrum of complement-mediated thrombotic microangiopathies: pathogenetic insights identifying novel treatment approaches

M Riedl, F Fakhouri, M Le Quintrec… - … in thrombosis and …, 2014‏ - thieme-connect.com
Thrombotic microangiopathy (TMA) is a rare but severe disorder characterized by
endothelial cell activation and thrombus formation. It manifests with the triad of hemolytic …